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Table 1 Patient characteristics

From: Hip pathologies in mucopolysaccharidosis type III

Characteristic

Total

Necrosis of femoral head

Correlation to necrosis

No

Yes

n = 32

n = 15 (46.9%)

n = 17 (53.1%)

Age (years)

 Mean ± SD

11.0 ± 5.7

11.1 ± 6.1

10.9 ± 5.4

 

 Range

 

3.3–27.0

3.4–23.6

Sex—no. (%)

 Male

21 (65.6)

8 (38.1)

13 (61.9)

p = 0.266

 Female

11 (34.4)

7 (63.6)

4 (36.4)

MPS subtype—no. (%)

 IIIA

26 (81.2)

13 (50.0)

13 (50.0)

p = 0.795

 IIIB

4 (12.5)

1 (25.0)

3 (75.0)

 IIIC

2 (6.2)

1 (50.0)

1 (50.0)

Phenotype—no./total no.(%)

 Severe

23/30 (76.7)

9 (39.1)

14 (60.9)

p = 0.036*

 Intermediate

7/30 (23.3)

6 (85.7)

1 (14.3)

Dysplasia—no. (%)

 No

23 (71.9)

13 (56.5)

10 (43.5)

p = 0.04*

 Yes

9 (28.1)

2 (22.2)

7 (77.8)

  1. No. number, SD standard deviation
  2. *Significant